Abstract

Hemiconvulsion-Hemiplegia-Epilepsy syndrome is characterized by a prolonged unilateral convulsion in the form of status producing a persisting hemiplegia during a febrile illness, followed by epilepsy. It occurs in a child, between 5 months and 4 years old, with a peak incidence during the first 2 years of life. Although the etiologies of this syndrome are diverse, preexisting asymptomatic lesion of perinatal or prenatal origin is found in a number of cases. I experienced a case of HHE syndrome in a 11 month old girl with abnormal perinatal history and developmental delay, who showed predominant right sided focal motor seizures followed by right hemiparesis.

• Keywords: Hemiconvulsion-Hemiplegia-Epilepsy syndrome;